Dissecting Aortic Aneurysm 55 Years after Diagnosis of Iris Flocculi
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چکیده
Purpose: The aim of this study is to report the clinical features, imaging studies, surgical removal, and pathology of congenital iris flocculi in a patient who developed a lifethreatening dissecting aortic aneurysm after 55 years of follow-up. Methods: Documentation with iris photography was performed from age 18 to 55 years, at which time anterior segment optical coherence tomography (OCT) was performed. At the time of subsequent cataract surgery, the iris flocculi were removed in each eye and submitted for light and electron microscopy. Results: The size and shape of the iris flocculi waxed and waned over the years but caused no visual disturbance. Anterior segment OCT demonstrated clear, round cysts with thin lining and no solid component. At the age of 55, congestive heart failure from a dissecting aortic aneurysm was discovered and surgically repaired. Subsequent bilateral cataract surgery and cyst removal were performed, and the iris flocculi were studied with light Received: January 19, 2016 Accepted after revision: March 19, 2016 Published online: April 21, 2016 Jerry A. Shields, MD Ocular Oncology Service, Suite 1440, Wills Eye Hospital 840 Walnut Street Philadelphia, PA 19107 (USA) E-Mail jerryashields @ gmail.com © 2016 S. Karger AG, Basel 2296–4681/16/0024–0222$39.50/0
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Dissecting Aortic Aneurysm 55 Years after Diagnosis of Iris Flocculi.
PURPOSE The aim of this study is to report the clinical features, imaging studies, surgical removal, and pathology of congenital iris flocculi in a patient who developed a life-threatening dissecting aortic aneurysm after 55 years of follow-up. METHODS Documentation with iris photography was performed from age 18 to 55 years, at which time anterior segment optical coherence tomography (OCT) w...
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